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Details on Person UniProt:P04275-2 VWF

Class:IdReferenceIsoform:8968618
_chainChangeLogsignal peptide:1-22 added on Fri February 17 2017;chain:23-763 added on Fri February 17 2017;chain:764-2813 added on Fri February 17 2017
_displayNameUniProt:P04275-2 VWF
_timestamp2024-11-03 19:39:36
chainsignal peptide:1-22
chain:23-763
chain:764-2813
checksumD5C1C78360917C29
commentFUNCTION Important in the maintenance of hemostasis, it promotes adhesion of platelets to the sites of vascular injury by forming a molecular bridge between sub-endothelial collagen matrix and platelet-surface receptor complex GPIb-IX-V. Also acts as a chaperone for coagulation factor VIII, delivering it to the site of injury, stabilizing its heterodimeric structure and protecting it from premature clearance from plasma.SUBUNIT Multimeric. Interacts with F8.INTERACTION Localized to storage granules.ALTERNATIVE PRODUCTS Plasma.DOMAIN The von Willebrand antigen 2 is required for multimerization of vWF and for its targeting to storage granules.PTM All cysteine residues are involved in intrachain or interchain disulfide bonds.PTM N- and O-glycosylated.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.SEQUENCE CAUTION Contaminating sequence. Sequence of unknown origin in the N-terminal part.ONLINE INFORMATION von Willebrand factor (vWF) mutation dbONLINE INFORMATION Von Willebrand factor entry
created[InstanceEdit:8964659] Weiser, JD
descriptionrecommendedName: von Willebrand factor shortName: vWF component recommendedName: von Willebrand antigen 2 alternativeName: von Willebrand antigen II /component
geneNameVWF
F8VWF
identifierP04275
isoformParent
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
Blood coagulation
Cell adhesion
Cleavage on pair of basic residues
Direct protein sequencing
Disease variant
Disulfide bond
Extracellular matrix
Glycoprotein
Hemostasis
Proteomics identification
Reference proteome
Repeat
Secreted
Signal
von Willebrand disease
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
nameVWF
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8957777] ENSEMBL:ENSG00000110799 VWF [Homo sapiens]
secondaryIdentifierVWF_HUMAN
Q8TCE8
Q99806
sequenceLength2813
species[Species:48887] Homo sapiens
variantIdentifierP04275-2
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