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Query author contributions in Reactome

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Details on Person UniProt:Q9Y3E5 PTRH2

Class:IdReferenceGeneProduct:67730
_chainChangeLogtransit peptide:1-62 added on Fri February 6 2015;chain:63-179 added on Fri February 6 2015;transit peptide:1-62 for 67730 removed on Fri August 11 2023;chain:63-179 for 67730 removed on Fri August 11 2023;chain:1-179 for 67730 added on Fri August 11 2023
_displayNameUniProt:Q9Y3E5 PTRH2
_timestamp2026-02-20 22:25:51
chainchain:1-179
checksum11A0BA9ECF6B5E46
commentFUNCTION Peptidyl-tRNA hydrolase which releases tRNAs from the ribosome during protein synthesis (PubMed:14660562). Promotes caspase-independent apoptosis by regulating the function of two transcriptional regulators, AES and TLE1.CATALYTIC ACTIVITY an N-acyl-L-alpha-aminoacyl-tRNA + H2O = an N-acyl-L-amino acid + a tRNA + H(+)SUBUNIT Monomer.SUBCELLULAR LOCATION Ubiquitinated by PRKN during mitophagy, leading to its degradation and enhancement of mitophagy. Deubiquitinated by USP30.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the PTH2 family.
descriptionrecommendedName: Peptidyl-tRNA hydrolase 2, mitochondrial shortName: PTH 2 ecNumber evidence="2"3.1.1.29 alternativeName: Bcl-2 inhibitor of transcription 1
geneNamePTRH2
BIT1
PTH2
CGI-147
identifierQ9Y3E5
isSequenceChangedFALSE
keyword3D-structure
Apoptosis
Disease variant
Hydrolase
Isopeptide bond
Membrane
Mitochondrion
Mitochondrion outer membrane
Proteomics identification
Reference proteome
Transmembrane
Transmembrane helix
Ubl conjugation
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9841277] Weiser, Joel
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9917590] Weiser, Joel, 2024-08-09
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
[InstanceEdit:9983091] Weiser, Joel, 2026-02-20
namePTRH2
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:9002571] ENSEMBL:ENSG00000141378 PTRH2 [Homo sapiens]
secondaryIdentifierPTH2_HUMAN
B3KUY4
Q9NTE5
sequenceLength179
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:5696909] PTRH2 [mitochondrial outer membrane] [Homo sapiens]
[EntityWithAccessionedSequence:6783190] PolyUb-PTRH2 [mitochondrial outer membrane] [Homo sapiens]
(referenceSequence)[GroupModifiedResidue:6783082] ubiquitinylated lysine (PolyUb [mitochondrial outer membrane]) at unknown position
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No pathways have been reviewed or authored by UniProt:Q9Y3E5 PTRH2 (67730)