Reactome: A Curated Pathway Database
THIS SITE IS USED FOR CURATION AND TESTING
IT IS NOT STABLE, IS LINKED TO AN INCOMPLETE DATA SET, AND IS NOT MONITORED FOR PERFORMANCE. WE STRONGLY RECOMMEND THE USE OF OUR PUBLIC SITE

Query author contributions in Reactome

Reactome depends on collaboration between our curation team and outside experts to assemble and peer-review its pathway modules. The integration of ORCID within Reactome enables us to meet a key challenge with authoring, curating and reviewing biological information by incentivizing and crediting the external experts that contribute their expertise and time to the Reactome curation process. More information is available at ORCID and Reactome.

If you have an ORCID ID that is not listed on this page, please forward this information to us and we will update your Reactome pathway records.

Name Email address

Details on Person UniProt:Q9BZK7 TBL1XR1

Class:IdReferenceGeneProduct:65719
_chainChangeLoginitiator methionine:1 added on Sat February 7 2015;chain:2-514 added on Sat February 7 2015;initiator methionine:1 for 65719 removed on Fri Nov 03 2023;initiator methionine: for 65719 added on Fri Nov 03 2023;initiator methionine: for 65719 removed on Fri Aug 15 2025;initiator methionine:1 for 65719 added on Fri Aug 15 2025
_displayNameUniProt:Q9BZK7 TBL1XR1
_timestamp2025-08-15 22:04:49
chaininitiator methionine:1
chain:2-514
checksum0B556D2EE4BA796D
commentFUNCTION F-box-like protein involved in the recruitment of the ubiquitin/19S proteasome complex to nuclear receptor-regulated transcription units. Plays an essential role in transcription activation mediated by nuclear receptors. Probably acts as integral component of the N-Cor corepressor complex that mediates the recruitment of the 19S proteasome complex, leading to the subsequent proteasomal degradation of N-Cor complex, thereby allowing cofactor exchange, and transcription activation.SUBUNIT Component of the N-Cor repressor complex, at least composed of NCOR1, NCOR2, HDAC3, TBL1X, TBL1XR1, CORO2A and GPS2 (PubMed:11931768). Probable component of some E3 ubiquitin ligase complex. Interacts with histones H2B and H4 (PubMed:12628926). Interacts with MECP2; bridges interaction between MECP2 and NCOR1 (By similarity). Interacts with USP44 (PubMed:27880911).INTERACTION Widely expressed including the pituitary, hypothalamus, white and brown adipose tissue, muscle and liver.DOMAIN The F-box-like domain is related to the F-box domain, and apparently displays the same function as component of ubiquitin E3 ligase complexes.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the WD repeat EBI family.SEQUENCE CAUTION Contaminating sequence. Potential poly-A sequence.
descriptionrecommendedName: F-box-like/WD repeat-containing protein TBL1XR1 alternativeName: Nuclear receptor corepressor/HDAC3 complex subunit TBLR1 alternativeName: TBL1-related protein 1 alternativeName: Transducin beta-like 1X-related protein 1
geneNameTBL1XR1
IRA1
TBLR1
identifierQ9BZK7
isSequenceChangedFALSE
keyword3D-structure
Acetylation
Activator
Chromatin regulator
Disease variant
Intellectual disability
Isopeptide bond
Nucleus
Phosphoprotein
Proteomics identification
Reference proteome
Repeat
Repressor
Transcription
Transcription regulation
Ubl conjugation
Ubl conjugation pathway
WD repeat
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9963647] Weiser, Joel, 2025-08-15
nameTBL1XR1
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8995169] ENSEMBL:ENSG00000177565 TBL1XR1 [Homo sapiens]
secondaryIdentifierTBL1R_HUMAN
D3DNQ9
Q14DC3
Q9H2I1
Q9H9A1
sequenceLength514
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:351643] TBL1XR1 [nucleoplasm] [Homo sapiens]
[Change default viewing format]
No pathways have been reviewed or authored by UniProt:Q9BZK7 TBL1XR1 (65719)