Reactome: A Curated Pathway Database
THIS SITE IS USED FOR CURATION AND TESTING
IT IS NOT STABLE, IS LINKED TO AN INCOMPLETE DATA SET, AND IS NOT MONITORED FOR PERFORMANCE. WE STRONGLY RECOMMEND THE USE OF OUR PUBLIC SITE

Query author contributions in Reactome

Reactome depends on collaboration between our curation team and outside experts to assemble and peer-review its pathway modules. The integration of ORCID within Reactome enables us to meet a key challenge with authoring, curating and reviewing biological information by incentivizing and crediting the external experts that contribute their expertise and time to the Reactome curation process. More information is available at ORCID and Reactome.

If you have an ORCID ID that is not listed on this page, please forward this information to us and we will update your Reactome pathway records.

Name Email address

Details on Person UniProt:P11498 PC

Class:IdReferenceGeneProduct:62537
_chainChangeLogtransit peptide:1-20 added on Sat February 7 2015;chain:21-1178 added on Sat February 7 2015
_displayNameUniProt:P11498 PC
_timestamp2025-02-21 19:00:47
chaintransit peptide:1-20
chain:21-1178
checksum381F527553A20095
commentFUNCTION Pyruvate carboxylase catalyzes a 2-step reaction, involving the ATP-dependent carboxylation of the covalently attached biotin in the first step and the transfer of the carboxyl group to pyruvate in the second. Catalyzes in a tissue specific manner, the initial reactions of glucose (liver, kidney) and lipid (adipose tissue, liver, brain) synthesis from pyruvate.CATALYTIC ACTIVITY hydrogencarbonate + pyruvate + ATP = oxaloacetate + ADP + phosphate + H(+)COFACTOR Binds 1 Mn(2+) ion per subunit.PATHWAY Carbohydrate biosynthesis; gluconeogenesis.SUBUNIT Homotetramer (PubMed:18297087). Interacts (via the biotin carboxylation domain) with SIRT4 (PubMed:23438705).INTERACTION Acetylation of Lys-748 might play a role in catalytic activity regulation.DISEASE The disease is caused by variants affecting the gene represented in this entry.ONLINE INFORMATION Pyruvate carboxylase entry
descriptionrecommendedName: fullName evidence="16"Pyruvate carboxylase, mitochondrial ecNumber evidence="13"6.4.1.1 alternativeName: Pyruvic carboxylase shortName: PCB
geneNamePC
identifierP11498
isSequenceChangedFALSE
keyword3D-structure
Acetylation
Alternative splicing
ATP-binding
Biotin
Disease variant
Gluconeogenesis
Ligase
Lipid biosynthesis
Lipid metabolism
Manganese
Metal-binding
Mitochondrion
Multifunctional enzyme
Nucleotide-binding
Phosphoprotein
Proteomics identification
Pyruvate
Reference proteome
Transit peptide
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
namePC
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8993256] ENSEMBL:ENSG00000173599 PC [Homo sapiens]
secondaryIdentifierPYC_HUMAN
B4DN00
Q16705
sequenceLength1178
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:8977163] UniProt:P11498-1 PC [Homo sapiens]
[ReferenceIsoform:8977164] UniProt:P11498-2 PC [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:2993804] Btn-PC [mitochondrial matrix] [Homo sapiens]
[EntityWithAccessionedSequence:3323119] PC [cytosol] [Homo sapiens]
[EntityWithAccessionedSequence:3323170] Btn-PC [cytosol] [Homo sapiens]
(referenceSequence)[ModifiedResidue:2993806] N6-biotinyl-L-lysine at 1144
[Change default viewing format]
No pathways have been reviewed or authored by UniProt:P11498 PC (62537)