Reactome: A Curated Pathway Database
THIS SITE IS USED FOR CURATION AND TESTING
IT IS NOT STABLE, IS LINKED TO AN INCOMPLETE DATA SET, AND IS NOT MONITORED FOR PERFORMANCE. WE STRONGLY RECOMMEND THE USE OF OUR PUBLIC SITE

Query author contributions in Reactome

Reactome depends on collaboration between our curation team and outside experts to assemble and peer-review its pathway modules. The integration of ORCID within Reactome enables us to meet a key challenge with authoring, curating and reviewing biological information by incentivizing and crediting the external experts that contribute their expertise and time to the Reactome curation process. More information is available at ORCID and Reactome.

If you have an ORCID ID that is not listed on this page, please forward this information to us and we will update your Reactome pathway records.

Name Email address

Details on Person UniProt:P30038 ALDH4A1

Class:IdReferenceGeneProduct:62513
_chainChangeLogtransit peptide:1-24 added on Fri February 6 2015;chain:25-563 added on Fri February 6 2015
_displayNameUniProt:P30038 ALDH4A1
_timestamp2025-02-21 19:15:16
chaintransit peptide:1-24
chain:25-563
checksum4D964771B7DB5FFD
commentFUNCTION Irreversible conversion of delta-1-pyrroline-5-carboxylate (P5C), derived either from proline or ornithine, to glutamate. This is a necessary step in the pathway interconnecting the urea and tricarboxylic acid cycles. The preferred substrate is glutamic gamma-semialdehyde, other substrates include succinic, glutaric and adipic semialdehydes.CATALYTIC ACTIVITY L-glutamate 5-semialdehyde + NAD(+) + H2O = L-glutamate + NADH + 2 H(+)BIOPHYSICOCHEMICAL PROPERTIES Amino-acid degradation; L-proline degradation into L-glutamate; L-glutamate from L-proline: step 2/2.SUBUNIT Homodimer.INTERACTION Highest expression is found in liver followed by skeletal muscle, kidney, heart, brain, placenta, lung and pancreas.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the aldehyde dehydrogenase family.
descriptionrecommendedName: Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial shortName: P5C dehydrogenase ecNumber: 1.2.1.88 alternativeName: Aldehyde dehydrogenase family 4 member A1 alternativeName: L-glutamate gamma-semialdehyde dehydrogenase
geneNameALDH4A1
ALDH4
P5CDH
identifierP30038
isSequenceChangedFALSE
keyword3D-structure
Acetylation
Alternative splicing
Direct protein sequencing
Disease variant
Mitochondrion
NAD
Oxidoreductase
Phosphoprotein
Proline metabolism
Proteomics identification
Reference proteome
Transit peptide
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
nameALDH4A1
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:9002191] ENSEMBL:ENSG00000159423 ALDH4A1 [Homo sapiens]
secondaryIdentifierAL4A1_HUMAN
A8K1Q7
B4DGE4
D2D4A3
Q16882
Q53HU4
Q5JNV6
Q8IZ38
Q96IF0
Q9UDI6
sequenceLength563
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:8974583] UniProt:P30038-1 ALDH4A1 [Homo sapiens]
[ReferenceIsoform:8974584] UniProt:P30038-2 ALDH4A1 [Homo sapiens]
[ReferenceIsoform:8974585] UniProt:P30038-3 ALDH4A1 [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:70673] ALDH4A1 [mitochondrial matrix] [Homo sapiens]
[Change default viewing format]
No pathways have been reviewed or authored by UniProt:P30038 ALDH4A1 (62513)