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Details on Person UniProt:O43272 PRODH

Class:IdReferenceGeneProduct:62190
_chainChangeLogtransit peptide:1- added on Fri February 6 2015;chain:-600 added on Fri February 6 2015
_displayNameUniProt:O43272 PRODH
_timestamp2025-02-21 19:00:35
chaintransit peptide:1-
chain:-600
checksum6283BBD016EFAA36
commentFUNCTION Converts proline to delta-1-pyrroline-5-carboxylate.CATALYTIC ACTIVITY L-proline + a quinone = (S)-1-pyrroline-5-carboxylate + a quinol + H(+)COFACTOR Amino-acid degradation; L-proline degradation into L-glutamate; L-glutamate from L-proline: step 1/2.SUBCELLULAR LOCATION Expressed in lung, skeletal muscle and brain, to a lesser extent in heart and kidney, and weakly in liver, placenta and pancreas.INDUCTION During p53/TP53-induced apoptosis.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE Disease susceptibility is associated with variants affecting the gene represented in this entry.SIMILARITY Belongs to the proline oxidase family.SEQUENCE CAUTION Artifact. Missing internal sequence that doesn't correspond to an exon-intron boundary.SEQUENCE CAUTION Intron retention. Includes intronic sequence at the 5' end.
descriptionrecommendedName: fullName evidence="15"Proline dehydrogenase 1, mitochondrial ecNumber evidence="7"1.5.5.2 alternativeName: Proline oxidase alternativeName: Proline oxidase 2 alternativeName: p53-induced gene 6 protein
geneNamePRODH
PIG6
POX2
PRODH2
identifierO43272
isSequenceChangedFALSE
keywordAcetylation
Alternative splicing
Disease variant
FAD
Flavoprotein
Mitochondrion
Oxidoreductase
Proline metabolism
Proteomics identification
Reference proteome
Schizophrenia
Transit peptide
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9917590] Weiser, Joel, 2024-08-09
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
namePRODH
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:9002565] ENSEMBL:ENSG00000100033 PRODH [Homo sapiens]
secondaryIdentifierPROD_HUMAN
A0A087WWM6
A6NF53
O14680
Q0P507
Q147W8
Q504W1
Q59FI8
Q6NV86
Q9UF13
sequenceLength600
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:243948] UniProt:O43272-2 PRODH [Homo sapiens]
[ReferenceIsoform:243950] UniProt:O43272-4 PRODH [Homo sapiens]
[ReferenceIsoform:401500] UniProt:O43272-1 PRODH [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:70668] PRODH [mitochondrial inner membrane] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:O43272 PRODH (62190)