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Query author contributions in Reactome

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Details on Person UniProt:Q93099 HGD

Class:IdReferenceGeneProduct:56492
_chainChangeLogchain:1-445 added on Fri February 6 2015
_displayNameUniProt:Q93099 HGD
_timestamp2024-11-03 19:46:07
chainchain:1-445
checksumF99B51C134FFF965
commentFUNCTION Catalyzes the conversion of homogentisate to maleylacetoacetate.CATALYTIC ACTIVITY homogentisate + O2 = 4-maleylacetoacetate + H(+)COFACTOR Amino-acid degradation; L-phenylalanine degradation; acetoacetate and fumarate from L-phenylalanine: step 4/6.SUBUNIT Homohexamer arranged as a dimer of trimers.INTERACTION Highest expression in the prostate, small intestine, colon, kidney and liver.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the homogentisate dioxygenase family.
descriptionrecommendedName: Homogentisate 1,2-dioxygenase ecNumber evidence="14"1.13.11.5 alternativeName: Homogentisate oxygenase alternativeName: Homogentisic acid oxidase alternativeName: Homogentisicase
geneNameHGD
HGO
identifierQ93099
isSequenceChangedFALSE
keyword3D-structure
Acetylation
Dioxygenase
Disease variant
Iron
Metal-binding
Oxidoreductase
Phenylalanine catabolism
Proteomics identification
Reference proteome
Tyrosine catabolism
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
nameHGD
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:9002985] ENSEMBL:ENSG00000113924 HGD [Homo sapiens]
secondaryIdentifierHGD_HUMAN
A8K417
B2R8Z0
sequenceLength445
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:71075] HGD [cytosol] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:Q93099 HGD (56492)