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Details on Person UniProt:P43026 GDF5

Class:IdReferenceGeneProduct:55528
_chainChangeLogsignal peptide:1-27 added on Sat February 7 2015;propeptide:28-381 added on Sat February 7 2015;chain:382-501 added on Sat February 7 2015
_displayNameUniProt:P43026 GDF5
_timestamp2025-02-21 19:07:01
chainsignal peptide:1-27
propeptide:28-381
chain:382-501
checksumFEBACCFBD7597C37
commentFUNCTION Growth factor involved in bone and cartilage formation. During cartilage development regulates differentiation of chondrogenic tissue through two pathways. Firstly, positively regulates differentiation of chondrogenic tissue through its binding of high affinity with BMPR1B and of less affinity with BMPR1A, leading to induction of SMAD1-SMAD5-SMAD8 complex phosphorylation and then SMAD protein signaling transduction (PubMed:15530414, PubMed:21976273, PubMed:24098149, PubMed:25092592). Secondly, negatively regulates chondrogenic differentiation through its interaction with NOG (PubMed:21976273). Required to prevent excessive muscle loss upon denervation. This function requires SMAD4 and is mediated by phosphorylated SMAD1/5/8 (By similarity). Binds bacterial lipopolysaccharide (LPS) and mediates LPS-induced inflammatory response, including TNF secretion by monocytes (PubMed:11276205).SUBUNIT Homodimer; disulfide-linked (By similarity). Interacts with serine proteases, HTRA1 and HTRA3 (By similarity). Following LPS binding, may form a complex with CXCR4, HSP90AA1 and HSPA8. Interacts with high affinity with NOG; inhibits chondrogenesis. Interacts with high affinity with BMPR1B and lower affinity with BMPR1A; positively regulates chondrocyte differentiation and induces SMAD dependent signaling. Interacts with FBN1 (via N-terminal domain) and FBN2 (PubMed:18339631). Interacts with TGFBR3 (PubMed:18184661).INTERACTION Predominantly expressed in long bones during embryonic development. Expressed in monocytes (at protein level).DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry. Some BDC patients with GDF5 mutations also manifest clinical features of ASPED angel-shaped phalango-epiphyseal dysplasia (ASPED), an autosomal dominant skeletal abnormality characterized by a typical angel-shaped phalanx, brachydactyly, specific radiological findings, abnormal dentition, hip dysplasia, and delayed bone age. This suggests that BDC and ASPED are part of the same clinical spectrum (PubMed:22828468).DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE Disease susceptibility is associated with variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the TGF-beta family.SEQUENCE CAUTION GDF5 entry
descriptionrecommendedName: Growth/differentiation factor 5 shortName: GDF-5 alternativeName: Bone morphogenetic protein 14 shortName: BMP-14 alternativeName: Cartilage-derived morphogenetic protein 1 shortName: CDMP-1 alternativeName: Lipopolysaccharide-associated protein 4 shortName: LAP-4 shortName: LPS-associated protein 4 alternativeName: Radotermin
geneNameGDF5
BMP14
CDMP1
identifierP43026
isSequenceChangedFALSE
keyword3D-structure
Cell membrane
Chondrogenesis
Cleavage on pair of basic residues
Cytokine
Disease variant
Disulfide bond
Dwarfism
Glycoprotein
Growth factor
Membrane
Proteomics identification
Reference proteome
Secreted
Signal
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9917590] Weiser, Joel, 2024-08-09
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
nameGDF5
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8990716] ENSEMBL:ENSG00000125965 GDF5 [Homo sapiens]
secondaryIdentifierGDF5_HUMAN
E1P5Q2
Q96SB1
sequenceLength501
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:2396129] GDF5(28-501) [extracellular region] [Homo sapiens]
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