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Query author contributions in Reactome

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Details on Person UniProt:Q9H2C0 GAN

Class:IdReferenceGeneProduct:55316
_chainChangeLogchain:1-597 added on Sat February 7 2015
_displayNameUniProt:Q9H2C0 GAN
_timestamp2024-11-03 19:41:02
chainchain:1-597
checksum4B6ECFA6849880C7
commentFUNCTION Probable cytoskeletal component that directly or indirectly plays an important role in neurofilament architecture. May act as a substrate-specific adapter of an E3 ubiquitin-protein ligase complex which mediates the ubiquitination and subsequent proteasomal degradation of target proteins. Controls degradation of TBCB. Controls degradation of MAP1B and MAP1S, and is critical for neuronal maintenance and survival.PATHWAY Protein modification; protein ubiquitination.SUBUNIT Interacts with TBCB. Interacts with CUL3. Part of a complex that contains CUL3, RBX1 and GAN. Interacts (via BTB domain) with UBA1. Interacts (via Kelch domains) with MAP1B (via C-terminus) and MAP1S (via C-terminus).INTERACTION Expressed in brain, heart and muscle.PTM Ubiquitinated by E3 ubiquitin ligase complex formed by CUL3 and RBX1 and probably targeted for proteasome-independent degradation.DISEASE The disease is caused by variants affecting the gene represented in this entry.
descriptionrecommendedName: Gigaxonin alternativeName: Kelch-like protein 16
geneNameGAN
GAN1
KLHL16
identifierQ9H2C0
isSequenceChangedFALSE
keyword3D-structure
Cytoplasm
Cytoskeleton
Disease variant
Kelch repeat
Neurodegeneration
Neuropathy
Proteomics identification
Reference proteome
Repeat
Ubl conjugation
Ubl conjugation pathway
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
nameGAN
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8997717] ENSEMBL:ENSG00000261609 GAN [Homo sapiens]
secondaryIdentifierGAN_HUMAN
sequenceLength597
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:976014] GAN [cytosol] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:Q9H2C0 GAN (55316)