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Details on Person UniProt:O75891 ALDH1L1

Class:IdReferenceGeneProduct:55022
_chainChangeLogchain:1-902 added on Sat February 7 2015
_displayNameUniProt:O75891 ALDH1L1
_timestamp2025-02-21 19:35:24
chainchain:1-902
checksumD92CB2930617F7CF
commentFUNCTION Cytosolic 10-formyltetrahydrofolate dehydrogenase that catalyzes the NADP(+)-dependent conversion of 10-formyltetrahydrofolate to tetrahydrofolate and carbon dioxide (PubMed:19933275, PubMed:21238436). May also have an NADP(+)-dependent aldehyde dehydrogenase activity towards formaldehyde, acetaldehyde, propionaldehyde, and benzaldehyde (By similarity).CATALYTIC ACTIVITY (6R)-10-formyltetrahydrofolate + NADP(+) + H2O = (6S)-5,6,7,8-tetrahydrofolate + CO2 + NADPH + H(+)SUBUNIT Homotetramer.INTERACTION Highly expressed in liver, pancreas and kidney.DOMAIN The N-terminal hydrolase domain has an NADP-independent formyltetrahydrofolate hydrolase activity, releasing formate and tetrahydrofolate.DOMAIN The C-terminal aldehyde dehydrogenase domain has an NADP-dependent dehydrogenase activity. It catalyzes the oxidation of formate, released by the hydrolysis of formyltetrahydrofolate, into CO2.DOMAIN The carrier domain is phosphopantetheinylated and uses the 4'-phosphopantetheine/4'-PP swinging arm to transfer the formyl group released by the N-terminal formyltetrahydrofolate hydrolase activity to the C-terminal aldehyde dehydrogenase domain that catalyzes its NADP-dependent oxidation into CO2. The overall NADP-dependent physiological reaction requires the 3 domains (N-terminal hydrolase, C-terminal aldehyde dehydrogenase and carrier domains) to convert formyltetrahydrofolate into tetrahydrofolate and CO2.PTM Phosphopantetheinylation at Ser-354 by AASDHPPT is required for the formyltetrahydrofolate dehydrogenase activity.SIMILARITY In the N-terminal section; belongs to the GART family.SIMILARITY In the C-terminal section; belongs to the aldehyde dehydrogenase family. ALDH1L subfamily.
descriptionrecommendedName: fullName evidence="16"Cytosolic 10-formyltetrahydrofolate dehydrogenase shortName: 10-FTHFDH shortName evidence="13"FDH ecNumber evidence="7 9"1.5.1.6 alternativeName: fullName evidence="17"Aldehyde dehydrogenase family 1 member L1
geneNameALDH1L1
FTHFD
identifierO75891
isSequenceChangedFALSE
keyword3D-structure
Acetylation
Alternative splicing
Cytoplasm
NADP
One-carbon metabolism
Oxidoreductase
Phosphopantetheine
Phosphoprotein
Proteomics identification
Reference proteome
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9862192] Weiser, Joel, 2024-02-26
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
nameALDH1L1
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8994041] ENSEMBL:ENSG00000144908 ALDH1L1 [Homo sapiens]
secondaryIdentifierAL1L1_HUMAN
B4DG36
E9PBX3
Q68CS1
Q8TBP8
sequenceLength902
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:8972692] UniProt:O75891-1 ALDH1L1 [Homo sapiens]
[ReferenceIsoform:8972693] UniProt:O75891-2 ALDH1L1 [Homo sapiens]
[ReferenceIsoform:8972694] UniProt:O75891-3 ALDH1L1 [Homo sapiens]
[ReferenceIsoform:8972695] UniProt:O75891-4 ALDH1L1 [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:6808507] ALDH1L1 [cytosol] [Homo sapiens]
(referenceSequence)[ModifiedResidue:6808486] O-phosphopantetheine-L-serine at 354
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No pathways have been reviewed or authored by UniProt:O75891 ALDH1L1 (55022)