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Details on Person UniProt:P37268 FDFT1

Class:IdReferenceGeneProduct:54742
_chainChangeLogchain:1-417 added on Fri February 6 2015
_displayNameUniProt:P37268 FDFT1
_timestamp2025-02-21 19:59:05
chainchain:1-417
checksumD36CBC8382F827EC
commentFUNCTION Catalyzes the condensation of 2 farnesyl pyrophosphate (FPP) moieties to form squalene. Proceeds in two distinct steps. In the first half-reaction, two molecules of FPP react to form the stable presqualene diphosphate intermediate (PSQPP), with concomitant release of a proton and a molecule of inorganic diphosphate. In the second half-reaction, PSQPP undergoes heterolysis, isomerization, and reduction with NADPH or NADH to form squalene. It is the first committed enzyme of the sterol biosynthesis pathway.CATALYTIC ACTIVITY 2 (2E,6E)-farnesyl diphosphate + NADPH + H(+) = squalene + 2 diphosphate + NADP(+)CATALYTIC ACTIVITY 2 (2E,6E)-farnesyl diphosphate + NADH + H(+) = squalene + 2 diphosphate + NAD(+)CATALYTIC ACTIVITY 2 (2E,6E)-farnesyl diphosphate = presqualene diphosphate + diphosphateCATALYTIC ACTIVITY presqualene diphosphate + NADH + H(+) = squalene + diphosphate + NAD(+)CATALYTIC ACTIVITY presqualene diphosphate + NADPH + H(+) = squalene + diphosphate + NADP(+)COFACTOR Terpene metabolism; lanosterol biosynthesis; lanosterol from farnesyl diphosphate: step 1/3.INTERACTION Widely expressed.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the phytoene/squalene synthase family.
descriptionrecommendedName: Squalene synthase shortName: SQS shortName: SS ecNumber evidence="3 6"2.5.1.21 alternativeName: FPP:FPP farnesyltransferase alternativeName: Farnesyl-diphosphate farnesyltransferase alternativeName: fullName evidence="12"Farnesyl-diphosphate farnesyltransferase 1
geneNameFDFT1
identifierP37268
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
Cholesterol biosynthesis
Cholesterol metabolism
Endoplasmic reticulum
Lipid biosynthesis
Lipid metabolism
Magnesium
Membrane
Metal-binding
Multifunctional enzyme
NAD
NADP
Proteomics identification
Reference proteome
Steroid biosynthesis
Steroid metabolism
Sterol biosynthesis
Sterol metabolism
Transferase
Transmembrane
Transmembrane helix
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
nameFDFT1
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:2393983] ENSEMBL:ENSG00000079459 FDFT1 [Homo sapiens]
secondaryIdentifierFDFT_HUMAN
B3KQ95
B4DJE5
B4DT56
B7Z1J3
Q96GT0
sequenceLength417
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:8969187] UniProt:P37268-1 FDFT1 [Homo sapiens]
[ReferenceIsoform:8969188] UniProt:P37268-2 FDFT1 [Homo sapiens]
[ReferenceIsoform:8969189] UniProt:P37268-3 FDFT1 [Homo sapiens]
[ReferenceIsoform:8969190] UniProt:P37268-4 FDFT1 [Homo sapiens]
[ReferenceIsoform:8969191] UniProt:P37268-5 FDFT1 [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:191369] FDFT1 [endoplasmic reticulum membrane] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:P37268 FDFT1 (54742)