Reactome: A Curated Pathway Database
THIS SITE IS USED FOR CURATION AND TESTING
IT IS NOT STABLE, IS LINKED TO AN INCOMPLETE DATA SET, AND IS NOT MONITORED FOR PERFORMANCE. WE STRONGLY RECOMMEND THE USE OF OUR PUBLIC SITE

Query author contributions in Reactome

Reactome depends on collaboration between our curation team and outside experts to assemble and peer-review its pathway modules. The integration of ORCID within Reactome enables us to meet a key challenge with authoring, curating and reviewing biological information by incentivizing and crediting the external experts that contribute their expertise and time to the Reactome curation process. More information is available at ORCID and Reactome.

If you have an ORCID ID that is not listed on this page, please forward this information to us and we will update your Reactome pathway records.

Name Email address

Details on Person UniProt:P15924 DSP

Class:IdReferenceGeneProduct:53556
_chainChangeLogchain:1-2871 added on Fri February 6 2015
_displayNameUniProt:P15924 DSP
_timestamp2026-02-20 21:38:52
chainchain:1-2871
checksum5770CC6B4F9F9F7B
commentFUNCTION A component of desmosome cell-cell junctions which are required for positive regulation of cellular adhesion (PubMed:25733715). Critical for cell-cell adhesion in early stage blastocysts and progression through proamniotic cavity formation (By similarity). Not required for preimplantation morphogenic process in blastocysts (By similarity). Required for keratin filament anchoring at the desmosome junction and subsequent organization of the keratin intermediate filament network within the cytoplasm (By similarity). Required for anchoring of desmosomes to the microtubule architecture, via its interaction with NIN (By similarity). Plays a key role in adhesion and organization of the dermal epithelial barrier (By similarity). Critical for the maintenance of the neural tube structure following formation and organization of the neuroepithelium (By similarity). Facilitates outgrowth and repair of motor neuron fibers in regenerating axons following injury, probably by promoting recruitment of a complex containing DSP, CDH2, VIM and JUP to the outgrowth tips (By similarity). Required for the normal formation of the heart, also required for development of vascular capillary structures and intact endothelial cell barriers (By similarity). Regulates profibrotic gene expression in cardiomyocytes via activation of the MAPK14/p38 MAPK signaling cascade and increase in TGFB1 protein abundance (By similarity). Maintains cardiac rhythmicity by ensuring correct cell-cell adhesion within the sinoatrial node, via stabilization of protein components of both desmosome and Gap junctions (By similarity). Involved in maintaining the protein stability and recruitment of GJA1 to functional gap junctions, via inhibition of KRAS-mediated MAPK1/MAPK3 phosphorylation of GJA1 (By similarity). Required for the survival and maintenance of germ cells in the gonads during embryonic development (By similarity). Binds to telomere DNA (via C-terminus) and acts to prevent telomere damage and maintain telomere length via its interaction with TRF2 (PubMed:31595153).SUBUNIT Homodimer. Identified in a complex containing at least DSP, JUP, VIM and CDH2; the complex is more abundant following crush injury in regenerating motor neurons and may promote axon outgrowth and motor fiber repair (By similarity). Interacts with COL17A1 (via cytoplasmic region) (PubMed:12482924). Interacts with DSC2 (PubMed:21062920). Interacts with PKP2 (PubMed:11790773, PubMed:22781308). Interacts with PKP1 (PubMed:10852826, PubMed:11790773, PubMed:23444369). Interacts weakly with TMEM65. Interacts with NIN: the interaction facilitates recruitment of NIN to desmosome cell-cell junctions (By similarity). Interacts with TRF2 in the nucleus; the interaction is required for DSP telomere binding (PubMed:31595153).INTERACTION Localizes to desmosome precursor particles in the cytoplasm (PubMed:25208567). Localizes to the cytoplasm in undifferentiated keratinocytes however becomes localizes to both lateral and tricellular cell-cell contacts as differentiation progresses and as epithelial sheet formation completes (By similarity). Localizes to the interface of the cortical keratin network and endodermal cell periphery in developing embryos (By similarity).ALTERNATIVE PRODUCTS Expressed in oral mucosa (at protein level) (PubMed:30479852). Expressed in arrector pili muscle (at protein level) (PubMed:29034528). Expressed in the heart in the heart (at protein level) (PubMed:18662195).TISSUE SPECIFICITY Apparently an obligate constituent of all desmosomes.TISSUE SPECIFICITY Resides predominantly in tissues and cells of stratified origin.DOMAIN The N-terminal region is required for localization to the desmosomal plaque and interacts with the N-terminal region of PKP1.PTM Methylation by PRMT1 promotes GSK3B-mediated phosphorylation cascade of multiple serine residues at the C-terminus resulting in trafficking to desmosome cell-cell junctions.PTM Phosphorylation by GSK3B occurs sequentially from Ser-2849 along multiple serine residue at the C-terminus. Hyperphosphorylation by GSK3B results in recruitment to desmosome cell-cell junction and promotion of intercellular adhesion (PubMed:25733715). Phosphorylation at Ser-2849 increases association with intermediate filament cytokeratin, potentially facilitating interaction between desmosome junctions and intermediate filament architecture (PubMed:33596089).DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.MISCELLANEOUS Minor isoform.SIMILARITY Belongs to the plakin or cytolinker family.ONLINE INFORMATION Desmoplakin entry
descriptionrecommendedName: fullName evidence="37"Desmoplakin shortName evidence="35"DP alternativeName: 250/210 kDa paraneoplastic pemphigus antigen
geneNameDSP
identifierP15924
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
Cardiomyopathy
Cell junction
Cell membrane
Cell projection
Coiled coil
Cytoplasm
Disease variant
DNA-binding
Epidermolysis bullosa
Membrane
Methylation
Nucleus
Palmoplantar keratoderma
Phosphoprotein
Proteomics identification
Reference proteome
Repeat
SH3 domain
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9909836] Weiser, Joel, 2024-05-14
[InstanceEdit:9917590] Weiser, Joel, 2024-08-09
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
[InstanceEdit:9983091] Weiser, Joel, 2026-02-20
nameDSP
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8992403] ENSEMBL:ENSG00000096696 DSP [Homo sapiens]
secondaryIdentifierDESP_HUMAN
B2RTT2
D7RX09
O75993
Q14189
Q9UHN4
sequenceLength2871
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:146308] UniProt:P15924-2 DSP [Homo sapiens]
[ReferenceIsoform:403017] UniProt:P15924-1 DSP [Homo sapiens]
[ReferenceIsoform:8965130] UniProt:P15924-3 DSP [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:201580] DSP [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:351843] DSP(?-?) [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:6801396] DSP [ficolin-1-rich granule membrane] [Homo sapiens]
[EntityWithAccessionedSequence:8847736] DSP [cornified envelope] [Homo sapiens]
[Change default viewing format]
No pathways have been reviewed or authored by UniProt:P15924 DSP (53556)