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Query author contributions in Reactome

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Details on Person UniProt:O94760 DDAH1

Class:IdReferenceGeneProduct:53496
_chainChangeLoginitiator methionine:1 added on Fri February 6 2015;chain:2-285 added on Fri February 6 2015;initiator methionine:1 for 53496 removed on Fri Nov 03 2023;initiator methionine: for 53496 added on Fri Nov 03 2023;initiator methionine: for 53496 removed on Fri Aug 15 2025;initiator methionine:1 for 53496 added on Fri Aug 15 2025
_displayNameUniProt:O94760 DDAH1
_timestamp2025-08-15 21:37:12
chaininitiator methionine:1
chain:2-285
checksumCD8875DF267EF39B
commentFUNCTION Hydrolyzes N(G),N(G)-dimethyl-L-arginine (ADMA) and N(G)-monomethyl-L-arginine (MMA) which act as inhibitors of NOS. Has therefore a role in the regulation of nitric oxide generation.CATALYTIC ACTIVITY N(omega),N(omega)-dimethyl-L-arginine + H2O = dimethylamine + L-citrullineCATALYTIC ACTIVITY N(omega)-methyl-L-arginine + H2O = L-citrulline + methylamineACTIVITY REGULATION Inhibited by zinc ions (By similarity). Enzyme purified in the absence of 1,10-phenanthroline contains on average 0.4 zinc atoms per subunit. Inhibited by 4-hydroxy-nonenal through the formation of a covalent adduct with His-173. Competitively inhibited by N(5)-iminopropyl-ornithine.BIOPHYSICOCHEMICAL PROPERTIES Optimum pH is 8.5.SUBUNIT Monomer.ALTERNATIVE PRODUCTS Detected in brain, liver, kidney and pancreas, and at low levels in skeletal muscle.SIMILARITY Belongs to the DDAH family.
descriptionrecommendedName: fullName evidence="10"N(G),N(G)-dimethylarginine dimethylaminohydrolase 1 shortName: DDAH-1 shortName: Dimethylarginine dimethylaminohydrolase 1 ecNumber evidence="4 5 6 7"3.5.3.18 alternativeName: DDAHI alternativeName: Dimethylargininase-1
geneNameDDAH1
DDAH
identifierO94760
isSequenceChangedFALSE
keyword3D-structure
Acetylation
Alternative splicing
Direct protein sequencing
Hydrolase
Metal-binding
Proteomics identification
Reference proteome
S-nitrosylation
Zinc
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9862192] Weiser, Joel, 2024-02-26
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
[InstanceEdit:9963647] Weiser, Joel, 2025-08-15
nameDDAH1
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8957972] ENSEMBL:ENSG00000153904 DDAH1 [Homo sapiens]
secondaryIdentifierDDAH1_HUMAN
Q5HYC8
Q86XK5
sequenceLength285
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:8976957] UniProt:O94760-1 DDAH1 [Homo sapiens]
[ReferenceIsoform:8976958] UniProt:O94760-2 DDAH1 [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:6783970] DDAH1 [cytosol] [Homo sapiens]
[EntityWithAccessionedSequence:8958304] DDAH1 [extracellular region] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:O94760 DDAH1 (53496)