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Details on Person UniProt:Q9UHC6 CNTNAP2

Class:IdReferenceGeneProduct:52978
_chainChangeLogsignal peptide:1-27 added on Fri February 6 2015;chain:28-1331 added on Fri February 6 2015
_displayNameUniProt:Q9UHC6 CNTNAP2
_timestamp2024-11-03 20:18:28
chainsignal peptide:1-27
chain:28-1331
checksumCFB2CB55BEFB99C2
commentFUNCTION Required for gap junction formation (Probable). Required, with CNTNAP1, for radial and longitudinal organization of myelinated axons. Plays a role in the formation of functional distinct domains critical for saltatory conduction of nerve impulses in myelinated nerve fibers. Demarcates the juxtaparanodal region of the axo-glial junction.SUBUNIT Interacts (via C-terminus) with KCNA2 (PubMed:10624965). Interacts with GPR37 (PubMed:25977097).INTERACTION Expressed in the juxtaparadonal region.ALTERNATIVE PRODUCTS Predominantly expressed in nervous system.DISEASE Disease susceptibility is associated with variants affecting the gene represented in this entry.DISEASE A chromosomal aberration involving CNTNAP2 is found in a patient with autism spectrum disorder. Paracentric inversion 46,XY,inv(7)(q11.22;q35). The inversion breakpoints disrupt the genes AUTS2 and CNTNAP2.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the neurexin family.SEQUENCE CAUTION Extended N-terminus.
descriptionrecommendedName: Contactin-associated protein-like 2 alternativeName: Cell recognition molecule Caspr2
geneNameCNTNAP2
CASPR2
KIAA0868
identifierQ9UHC6
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
Autism
Autism spectrum disorder
Cell adhesion
Cell junction
Cell projection
Chromosomal rearrangement
Disulfide bond
EGF-like domain
Epilepsy
Glycoprotein
Intellectual disability
Membrane
Phosphoprotein
Proteomics identification
Reference proteome
Repeat
Signal
Transmembrane
Transmembrane helix
modified[InstanceEdit:84067] Schmidt, EE, 2003-12-18 04:29:09
[InstanceEdit:143527] Schmidt, EE, 2004-11-12 07:45:10
[InstanceEdit:217385] Schmidt, EE, 2008-03-27 06:23:53
[InstanceEdit:354386] Schmidt, EE, 2008-06-18 04:45:12
[InstanceEdit:384350] Kanapin, AA, 2008-11-26 14:00:39
[InstanceEdit:392885] Kanapin, AA, 2009-03-09 12:07:18
[InstanceEdit:400710] Schmidt, EE, 2009-03-25 05:33:35
[InstanceEdit:423310] Kanapin, AA
[InstanceEdit:435478] Kanapin, AA
[InstanceEdit:435871] Kanapin, AA
[InstanceEdit:447347] Kanapin, AA
[InstanceEdit:525883] Kanapin, AA
[InstanceEdit:613449] Kanapin, AA
[InstanceEdit:797602] Kanapin, AA
[InstanceEdit:937368] Yung, CK
[InstanceEdit:1042053] Yung, CK
[InstanceEdit:1220657] Yung, CK
[InstanceEdit:1300696] Yung, CK
[InstanceEdit:1301627] Yung, CK
[InstanceEdit:1551960] Weiser, JD
[InstanceEdit:1995863] Weiser, JD
[InstanceEdit:2132304] Weiser, JD
[InstanceEdit:2265580] Weiser, JD
[InstanceEdit:3445779] Weiser, JD
[InstanceEdit:4341137] Weiser, JD
[InstanceEdit:5433710] Weiser, JD
[InstanceEdit:5618415] Weiser, JD
[InstanceEdit:5634237] Weiser, JD
[InstanceEdit:5673015] Weiser, JD
[InstanceEdit:6791590] Weiser, JD
[InstanceEdit:8987656] Weiser, JD
[InstanceEdit:9015733] Weiser, JD
[InstanceEdit:9037114] Weiser, JD
[InstanceEdit:9627708] Weiser, JD
[InstanceEdit:9637257] Weiser, JD
[InstanceEdit:9676415] Weiser, JD
[InstanceEdit:9715482] Weiser, JD
[InstanceEdit:9730071] Weiser, JD
[InstanceEdit:9796772] Weiser, Joel
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9862192] Weiser, Joel, 2024-02-26
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
nameCNTNAP2
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8999401] ENSEMBL:ENSG00000174469 CNTNAP2 [Homo sapiens]
secondaryIdentifierCNTP2_HUMAN
D3DWG2
Q14DG2
Q52LV1
Q5H9Q7
Q9UQ12
sequenceLength1331
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:224724] UniProt:Q9UHC6-2 CNTNAP2 [Homo sapiens]
[ReferenceIsoform:415364] UniProt:Q9UHC6-1 CNTNAP2 [Homo sapiens]
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