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Details on Person UniProt:P04114 APOB

Class:IdReferenceGeneProduct:50108
_chainChangeLogsignal peptide:1-27 added on Fri February 6 2015;chain:28-4563 added on Fri February 6 2015;chain:28-2179 added on Fri February 6 2015
_displayNameUniProt:P04114 APOB
_timestamp2025-05-21 21:41:09
chainsignal peptide:1-27
chain:28-4563
chain:28-2179
checksumD1073B2D5172A370
commentFUNCTION Apolipoprotein B is a major protein constituent of chylomicrons (apo B-48), LDL (apo B-100) and VLDL (apo B-100). Apo B-100 functions as a recognition signal for the cellular binding and internalization of LDL particles by the apoB/E receptor.SUBUNIT Interacts with PCSK9 (PubMed:22580899). Interacts with MTTP (PubMed:26224785, PubMed:27206948). Interacts with AUP1 (PubMed:28183703). Interacts with CIDEB (By similarity).INTERACTION Up-regulated in response to enterovirus 71 (EV71) infection (at protein level).PTM Palmitoylated; structural requirement for proper assembly of the hydrophobic core of the lipoprotein particle.RNA EDITING The stop codon (UAA) at position 2180 is created by an APOBEC1-containing mRNA editing complex. Apo B-48, derived from the fully edited RNA, is produced only in the intestine and is found in chylomicrons. Apo B-48 is a shortened form of apo B-100 which lacks the LDL-receptor region. The unedited version (apo B-100) is produced by the liver and is found in the VLDL and LDL.POLYMORPHISM Genetic variations in APOB define the low density lipoprotein cholesterol level quantitative trait locus 4 (LDLCQ4) [MIM:615558].DISEASE The disease is caused by variants affecting the gene represented in this entry. Most cases of FHBL1 result from nonsense mutations in the APOB gene that lead to a premature stop codon, which generate prematurely truncated apo B protein products (PubMed:21981844).DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE Defects in APOB associated with defects in other genes (polygenic) can contribute to hypocholesterolemia.SEQUENCE CAUTION Apolipoprotein B entry
descriptionrecommendedName: Apolipoprotein B-100 shortName: Apo B-100 component recommendedName: Apolipoprotein B-48 shortName: Apo B-48 /component
geneNameAPOB
identifierP04114
isSequenceChangedFALSE
keyword3D-structure
Acetylation
Atherosclerosis
Cholesterol metabolism
Chylomicron
Cytoplasm
Direct protein sequencing
Disease variant
Disulfide bond
Glycoprotein
Heparin-binding
LDL
Lipid droplet
Lipid metabolism
Lipid transport
Lipoprotein
Palmitate
Phosphoprotein
Proteomics identification
Reference proteome
RNA editing
Secreted
Signal
Steroid metabolism
Sterol metabolism
Transport
VLDL
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9862192] Weiser, Joel, 2024-02-26
[InstanceEdit:9909836] Weiser, Joel, 2024-05-14
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9948485] Weiser, Joel, 2025-05-21
nameAPOB
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8958374] ENSEMBL:ENSG00000084674 APOB [Homo sapiens]
secondaryIdentifierAPOB_HUMAN
O00502
P78479
P78480
P78481
Q13779
Q13785
Q13786
Q13787
Q13788
Q4ZG63
Q53QC8
Q7Z600
Q9UMN0
sequenceLength4563
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:171065] APOB(28-4563) [extracellular region] [Homo sapiens]
[EntityWithAccessionedSequence:171089] APOB(28-4563) [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:171119] APOB(28-4563) [endosome lumen] [Homo sapiens]
[EntityWithAccessionedSequence:171121] APOB(28-4563) [endosome membrane] [Homo sapiens]
[EntityWithAccessionedSequence:171155] APOB(28-4563) [clathrin-coated endocytic vesicle membrane] [Homo sapiens]
[EntityWithAccessionedSequence:174620] APOB(28-2179) [endoplasmic reticulum lumen] [Homo sapiens]
[EntityWithAccessionedSequence:174625] APOB(28-2179) [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:174637] APOB(28-2179) [endoplasmic reticulum membrane] [Homo sapiens]
[EntityWithAccessionedSequence:174716] APOB(28-2179) [endosome lumen] [Homo sapiens]
[EntityWithAccessionedSequence:174762] APOB(28-2179) [endosome membrane] [Homo sapiens]
List all 25 refering instances
(referenceSequence)[ModifiedResidue:2173695] dihydroxyphenylalanine (Phe) at 4380
[ModifiedResidue:2173697] L-tyrosine residue at 883
[ModifiedResidue:2173698] modified L-lysine residue at 2208
[ModifiedResidue:2173700] Oxohistidine (from histidine) at 596
[ModifiedResidue:2173703] glutamyl semialdehyde (Pro) at 3293
[ModifiedResidue:2173704] Oxohistidine (from histidine) at 2507
[ModifiedResidue:2173706] dihydroxyphenylalanine (Phe) at 276
[ModifiedResidue:2173707] glutamyl semialdehyde (Pro) at 2659
[ModifiedResidue:2173710] Oxohistidine (from histidine) at 4529
[ModifiedResidue:2173711] L-tyrosine residue at 2665
List all 34 refering instances
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No pathways have been reviewed or authored by UniProt:P04114 APOB (50108)