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Details on Person UniProt:O00116 AGPS

Class:IdReferenceGeneProduct:49700
_chainChangeLogtransit peptide:1-58 added on Sat February 7 2015;chain:59-658 added on Sat February 7 2015
_displayNameUniProt:O00116 AGPS
_timestamp2025-02-21 18:33:35
chaintransit peptide:1-58
chain:59-658
checksum0E97AE86B513DF32
commentFUNCTION Catalyzes the exchange of the acyl chain in acyl-dihydroxyacetonephosphate (acyl-DHAP) for a long chain fatty alcohol, yielding the first ether linked intermediate, i.e. alkyl-dihydroxyacetonephosphate (alkyl-DHAP), in the pathway of ether lipid biosynthesis.CATALYTIC ACTIVITY a long chain fatty alcohol + a 1-acylglycerone 3-phosphate = a 1-O-alkylglycerone 3-phosphate + a long-chain fatty acid + H(+)CATALYTIC ACTIVITY hexadecan-1-ol + 1-hexadecanoylglycerone 3-phosphate = 1-O-hexadecylglycerone 3-phosphate + hexadecanoate + H(+)CATALYTIC ACTIVITY 1-hexadecanoylglycerone 3-phosphate + a long-chain fatty acid = a 1-acylglycerone 3-phosphate + hexadecanoateCOFACTOR Glycerolipid metabolism; ether lipid biosynthesis.SUBUNIT Homodimer.INTERACTION The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the FAD-binding oxidoreductase/transferase type 4 family.
descriptionrecommendedName: Alkyldihydroxyacetonephosphate synthase, peroxisomal shortName: Alkyl-DHAP synthase ecNumber evidence="8 9"2.5.1.26 alternativeName: Aging-associated gene 5 protein alternativeName: Alkylglycerone-phosphate synthase
geneNameAGPS
AAG5
identifierO00116
isSequenceChangedFALSE
keywordAcetylation
Cataract
Disease variant
Dwarfism
FAD
Flavoprotein
Lipid biosynthesis
Lipid metabolism
Membrane
Peroxisome
Phosphoprotein
Proteomics identification
Reference proteome
Rhizomelic chondrodysplasia punctata
Transferase
Transit peptide
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
nameAGPS
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:9002187] ENSEMBL:ENSG00000018510 AGPS [Homo sapiens]
secondaryIdentifierADAS_HUMAN
A5D8U9
Q2TU35
sequenceLength658
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:49699] AGPS [peroxisomal matrix] [Homo sapiens]
[EntityWithAccessionedSequence:9033119] AGPS(1-658) [cytosol] [Homo sapiens]
[EntityWithAccessionedSequence:9033519] AGPS(1-58) [peroxisomal matrix] [Homo sapiens]
[EntityWithAccessionedSequence:9033523] AGPS(1-658) [peroxisomal matrix] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:O00116 AGPS (49700)