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Details on Person UniProt:Q9Y2Q0 ATP8A1

Class:IdReferenceGeneProduct:49342
_chainChangeLogchain:1-1164 added on Fri February 6 2015
_displayNameUniProt:Q9Y2Q0 ATP8A1
_timestamp2026-02-20 22:19:04
chainchain:1-1164
checksumCE1EAF0206CD36F7
commentFUNCTION Catalytic component of a P4-ATPase flippase complex which catalyzes the hydrolysis of ATP coupled to the transport of aminophospholipids from the outer to the inner leaflet of various membranes and ensures the maintenance of asymmetric distribution of phospholipids (PubMed:31416931). Phospholipid translocation also seems to be implicated in vesicle formation and in uptake of lipid signaling molecules. In vitro, its ATPase activity is selectively and stereospecifically stimulated by phosphatidylserine (PS) (PubMed:31416931). The flippase complex ATP8A1:TMEM30A seems to play a role in regulation of cell migration probably involving flippase-mediated translocation of phosphatidylethanolamine (PE) at the cell membrane (By similarity). Acts as aminophospholipid translocase at the cell membrane in neuronal cells (By similarity).CATALYTIC ACTIVITY ATP + H2O + phospholipidSide 1 = ADP + phosphate + phospholipidSide 2.CATALYTIC ACTIVITY a 1,2-diacyl-sn-glycero-3-phospho-L-serine(out) + ATP + H2O = a 1,2-diacyl-sn-glycero-3-phospho-L-serine(in) + ADP + phosphate + H(+)COFACTOR ATPase activity is stimulated by phosphatidylserine (PS) and minimally by phosphatidylethanolamine (PE). ATPase activity is inhibited by beryllium fluoride and aluminum trifluoride (PubMed:31416931).BIOPHYSICOCHEMICAL PROPERTIES Component of a P4-ATPase flippase complex which consists of a catalytic alpha subunit and an accessory beta subunit (PubMed:31416931). Interacts with TMEM30A to form a flippase complex; this complex forms an intermediate phosphoenzyme (PubMed:20947505, PubMed:20961850, PubMed:21914794, PubMed:31416931). Interacts with TMEM30B; this interaction is reported conflictingly (PubMed:20961850).SUBCELLULAR LOCATION Exit from the endoplasmic reticulum requires the presence of TMEM30A, but not TMEM30B (PubMed:20947505). In the presence of TMEM30A, predominantly located in cytoplasmic punctate structures and localizes to the cell membrane (PubMed:20947505). Localizes to plasma membranes of red blood cells (By similarity).ALTERNATIVE PRODUCTS Found in most adult tissues except liver, testis and placenta. Most abundant in heart, brain and skeletal muscle. Also detected in fetal tissues. Isoform 1 is only detected in brain, skeletal muscle and heart and is the most abundant form in skeletal muscle. Highly expressed in platelets (PubMed:30674456).PTM Cleaved by calpain in a caspase- and calcium influx-dependent manner during platelet apoptosis leading to a 100 kDa polypeptide.SIMILARITY Belongs to the cation transport ATPase (P-type) (TC 3.A.3) family. Type IV subfamily.SEQUENCE CAUTION Truncated N-terminus.SEQUENCE CAUTION Truncated N-terminus.
descriptionrecommendedName: fullName evidence="14"Phospholipid-transporting ATPase IA ecNumber evidence="4"7.6.2.1 alternativeName: ATPase class I type 8A member 1 alternativeName: Chromaffin granule ATPase II alternativeName: P4-ATPase flippase complex alpha subunit ATP8A1
geneNameATP8A1
ATPIA
identifierQ9Y2Q0
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
ATP-binding
Cell membrane
Cytoplasmic vesicle
Endoplasmic reticulum
Golgi apparatus
Lipid transport
Magnesium
Membrane
Metal-binding
Nucleotide-binding
Phosphoprotein
Proteomics identification
Reference proteome
Translocase
Transmembrane
Transmembrane helix
Transport
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9841277] Weiser, Joel
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
[InstanceEdit:9948485] Weiser, Joel, 2025-05-21
[InstanceEdit:9983091] Weiser, Joel, 2026-02-20
nameATP8A1
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8989978] ENSEMBL:ENSG00000124406 ATP8A1 [Homo sapiens]
secondaryIdentifierAT8A1_HUMAN
Q32M35
Q32M36
Q4W5J7
Q4W5P2
sequenceLength1164
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:143670] UniProt:Q9Y2Q0-2 ATP8A1 [Homo sapiens]
[ReferenceIsoform:415964] UniProt:Q9Y2Q0-1 ATP8A1 [Homo sapiens]
[ReferenceIsoform:8966894] UniProt:Q9Y2Q0-3 ATP8A1 [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:939739] ATP8A1 [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:6799530] ATP8A1 [specific granule membrane] [Homo sapiens]
[EntityWithAccessionedSequence:6801000] ATP8A1 [azurophil granule membrane] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:Q9Y2Q0 ATP8A1 (49342)