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Details on Person UniProt:Q93008-1 USP9X

Class:IdReferenceIsoform:412531
_chainChangeLogchain:1-2570 added on Fri February 6 2015;chain:1-2570 for 412531 removed on Thu November 5 2020;chain:1-2554 for 412531 added on Thu November 5 2020
_displayNameUniProt:Q93008-1 USP9X
_timestamp2024-11-03 20:17:21
chainchain:1-2554
checksum16B87B7FCC1428AF
commentFUNCTION Deubiquitinase involved both in the processing of ubiquitin precursors and of ubiquitinated proteins (PubMed:18254724, PubMed:19135894, PubMed:22371489, PubMed:25944111, PubMed:29626158, PubMed:30914461, PubMed:37454738). May therefore play an important regulatory role at the level of protein turnover by preventing degradation of proteins through the removal of conjugated ubiquitin (PubMed:18254724, PubMed:19135894, PubMed:22371489, PubMed:25944111, PubMed:29626158, PubMed:30914461, PubMed:37454738). Specifically hydrolyzes 'Lys-11'-, followed by 'Lys-63'-, 'Lys-48'- and 'Lys-6'-linked polyubiquitins chains (PubMed:30914461). Essential component of TGF-beta/BMP signaling cascade (PubMed:19135894). Specifically deubiquitinates monoubiquitinated SMAD4, opposing the activity of E3 ubiquitin-protein ligase TRIM33 (PubMed:19135894). Deubiquitinates alkylation repair enzyme ALKBH3 (PubMed:25944111). OTUD4 recruits USP7 and USP9X to stabilize ALKBH3, thereby promoting the repair of alkylated DNA lesions (PubMed:25944111). Deubiquitinates RNA demethylase enzyme ALKBH5, promoting its stability (PubMed:37454738). Deubiquitinates mTORC2 complex component RICTOR at 'Lys-294' by removing 'Lys-63'-linked polyubiquitin chains, stabilizing RICTOR and enhancing its binding to MTOR, thus promoting mTORC2 complex assembly (PubMed:33378666). Regulates chromosome alignment and segregation in mitosis by regulating the localization of BIRC5/survivin to mitotic centromeres (PubMed:16322459). Involved in axonal growth and neuronal cell migration (PubMed:24607389). Regulates cellular clock function by enhancing the protein stability and transcriptional activity of the core circadian protein BMAL1 via its deubiquitinating activity (PubMed:29626158). Acts as a regulator of peroxisome import by mediating deubiquitination of PEX5: specifically deubiquitinates PEX5 monoubiquitinated at 'Cys-11' following its retrotranslocation into the cytosol, resetting PEX5 for a subsequent import cycle (PubMed:22371489). Deubiquitinates PEG10 (By similarity). Inhibits the activation of the Hippo signaling pathway via deubiquitination of AMOTL2 at 'Lys-347' and 'Lys-408' which prohibits its interaction with and activation of LATS2. Loss of LATS2 activation and subsequent loss of YAP1 phosphorylation results in an increase in YAP1-driven transcription of target genes (PubMed:26598551, PubMed:34404733).CATALYTIC ACTIVITY Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal).SUBUNIT Interacts with SMAD4, MARK4, NUAK1 and BIRC5/survivin (PubMed:16322459, PubMed:18254724, PubMed:19135894). Interacts with DCX (PubMed:24607389). Interacts with OTUD4 and USP7; the interaction is direct (PubMed:25944111).INTERACTION Widely expressed in embryonic and adult tissues.INDUCTION By growth factors.DISEASE The disease may be caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.MISCELLANEOUS Escapes X-inactivation.SIMILARITY Belongs to the peptidase C19 family.
created[InstanceEdit:400710] Schmidt, EE, 2009-03-25 05:33:35
descriptionrecommendedName: Ubiquitin carboxyl-terminal hydrolase 9X ecNumber evidence="7 8 11 12 14 15 18"3.4.19.12 alternativeName: Deubiquitinating enzyme FAF-X alternativeName: Fat facets in mammals shortName: hFAM alternativeName: Fat facets protein-related, X-linked alternativeName: Ubiquitin thioesterase FAF-X alternativeName: Ubiquitin-specific protease 9, X chromosome alternativeName: Ubiquitin-specific-processing protease FAF-X
geneNameUSP9X
DFFRX
FAM
USP9
identifierQ93008
isoformParent
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
Biological rhythms
Cell cycle
Cell division
Cell projection
Chromosome partition
Cytoplasm
Cytoskeleton
Disease variant
Hydrolase
Intellectual disability
Mitosis
Phosphoprotein
Protease
Proteomics identification
Reference proteome
Thiol protease
Ubl conjugation pathway
Zinc
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9917590] Weiser, Joel, 2024-08-09
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
nameUSP9X
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8960200] ENSEMBL:ENSG00000124486 USP9X [Homo sapiens]
secondaryIdentifierUSP9X_HUMAN
O75550
Q8WWT3
Q8WX12
sequenceLength2554
species[Species:48887] Homo sapiens
variantIdentifierQ93008-1
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No pathways have been reviewed or authored by UniProt:Q93008-1 USP9X (412531)