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Details on Person UniProt:Q8IXI1 RHOT2

Class:IdReferenceGeneProduct:410886
_chainChangeLogchain:1-618 added on Sat February 7 2015
_displayNameUniProt:Q8IXI1 RHOT2
_timestamp2025-08-15 22:01:55
chainchain:1-618
checksumC72ECBCA33D04B6B
commentFUNCTION Atypical mitochondrial nucleoside-triphosphatase (NTPase) involved in mitochondrial trafficking (PubMed:16630562, PubMed:22396657, PubMed:30513825). Probably involved in control of anterograde transport of mitochondria and their subcellular distribution (PubMed:22396657). Can hydrolyze GTP (By similarity). Can hydrolyze ATP and UTP (PubMed:30513825).CATALYTIC ACTIVITY GTP + H2O = GDP + phosphate + H(+)CATALYTIC ACTIVITY ATP + H2O = ADP + phosphate + H(+)CATALYTIC ACTIVITY UTP + H2O = UDP + phosphate + H(+)SUBUNIT Homodimer (PubMed:27605430). Interacts with the kinesin-binding proteins TRAK1/OIP106 and TRAK2/GRIF1, forming a link between mitochondria and the trafficking apparatus of the microtubules (PubMed:16630562). Interacts with ARMCX3 (By similarity). Found in a complex with KIF5B, OGT, RHOT1 and TRAK1 (PubMed:24995978).INTERACTION Colocalizes with MGARP and RHOT2 at the mitochondria.ALTERNATIVE PRODUCTS Ubiquitously expressed. Highly expressed in heart, liver, skeletal muscle, kidney and pancreas.DOMAIN The Miro 2 domain is necessary for efficient ubiquitination by PRKN.PTM Ubiquitinated by PRKN in a PINK1-dependent manner, leading to its degradation.SIMILARITY Belongs to the mitochondrial Rho GTPase family.SEQUENCE CAUTION Extended N-terminus.SEQUENCE CAUTION Extended N-terminus.
created[InstanceEdit:400710] Schmidt, EE, 2009-03-25 05:33:35
descriptionrecommendedName: Mitochondrial Rho GTPase 2 shortName: MIRO-2 shortName: hMiro-2 ecNumber evidence="1"3.6.5.- alternativeName: Ras homolog gene family member T2
geneNameRHOT2
ARHT2
C16orf39
identifierQ8IXI1
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
Calcium
GTP-binding
Hydrolase
Isopeptide bond
Magnesium
Membrane
Metal-binding
Mitochondrion
Mitochondrion outer membrane
Nucleotide-binding
Proteomics identification
Reference proteome
Repeat
Transmembrane
Transmembrane helix
Ubl conjugation
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9963647] Weiser, Joel, 2025-08-15
nameRHOT2
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:9000695] ENSEMBL:ENSG00000140983 RHOT2 [Homo sapiens]
secondaryIdentifierMIRO2_HUMAN
A2IDC2
Q8NF53
Q96C13
Q96S17
Q9BT60
Q9H7M8
sequenceLength618
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:194860] UniProt:Q8IXI1-2 RHOT2 [Homo sapiens]
[ReferenceIsoform:194903] UniProt:Q8IXI1-1 RHOT2 [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:3006729] RHOT2 [cytosol] [Homo sapiens]
[EntityWithAccessionedSequence:3006730] RHOT2 [mitochondrial outer membrane] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:Q8IXI1 RHOT2 (410886)