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Details on Person UniProt:Q9BX79 STRA6

Class:IdReferenceGeneProduct:249777
_chainChangeLogchain:1-667 added on Fri February 6 2015
_displayNameUniProt:Q9BX79 STRA6
_timestamp2024-11-03 19:54:10
chainchain:1-667
checksumD20840A46998BA2E
commentFUNCTION Functions as a retinol transporter. Accepts all-trans retinol from the extracellular retinol-binding protein RBP4, facilitates retinol transport across the cell membrane, and then transfers retinol to the cytoplasmic retinol-binding protein RBP1 (PubMed:18316031, PubMed:22665496, PubMed:9452451). Retinol uptake is enhanced by LRAT, an enzyme that converts retinol to all-trans retinyl esters, the storage forms of vitamin A (PubMed:18316031, PubMed:22665496). Contributes to the activation of a signaling cascade that depends on retinol transport and LRAT-dependent generation of retinol metabolites that then trigger activation of JAK2 and its target STAT5, and ultimately increase the expression of SOCS3 and inhibit cellular responses to insulin (PubMed:21368206, PubMed:22665496). Important for the homeostasis of vitamin A and its derivatives, such as retinoic acid (PubMed:18316031). STRA6-mediated transport is particularly important in the eye, and under conditions of dietary vitamin A deficiency (Probable). Does not transport retinoic acid (PubMed:18316031).SUBUNIT Homodimer (By similarity). Interacts with JAK2 and STAT5 (PubMed:21368206). Interacts (via extracellular domains) with RBP4 (PubMed:22665496). Interacts (via cytoplasmic domains) with RBP1 (PubMed:22665496).INTERACTION In the retinal pigment epithelium localizes to the basolateral membrane.ALTERNATIVE PRODUCTS Broad expression. In adult eye expressed in sclera, retina, retinal pigment epithelium, and trabecular meshwork but not in choroid and iris.INDUCTION Up-regulated in the colorectal cancer cell line WiDr by the administration of retinoic acid and in tumors with frequent defects in Wnt-1 signaling.DOMAIN Contrary to predictions, contains nine transmembrane helices, with an extracellular N-terminus and a cytoplasmic C-terminus (By similarity). Besides, contains one long helix that dips into the membrane and then runs more or less parallel to the membrane surface (By similarity).PTM Phosphorylated on tyrosine residues in response to RBP4 binding (PubMed:21368206, PubMed:22665496). Phosphorylation requires the presence of LRAT, suggesting it may be triggered by the uptake of retinol that is then metabolized within the cell to retinoids that function as signaling molecules (PubMed:22665496).DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE Mutations in STRA6 may be a cause of isolated colobomatous microphthalmia, a disorder of the eye characterized by an abnormally small ocular globe.SEQUENCE CAUTION Truncated N-terminus.SEQUENCE CAUTION Extended N-terminus.SEQUENCE CAUTION Extended N-terminus.
created[InstanceEdit:217385] Schmidt, EE, 2008-03-27 06:23:53
descriptionrecommendedName: Receptor for retinol uptake STRA6 alternativeName: fullName evidence="24 26"Retinol-binding protein receptor STRA6 alternativeName: Stimulated by retinoic acid gene 6 protein homolog
geneNameSTRA6
PP14296
UNQ3126/PRO10282/PRO19578
identifierQ9BX79
isSequenceChangedFALSE
keywordAlternative splicing
Cell membrane
Disease variant
Glycoprotein
Membrane
Microphthalmia
Phosphoprotein
Proteomics identification
Receptor
Reference proteome
Retinol-binding
Transmembrane
Transmembrane helix
Transport
Vitamin A
modified[InstanceEdit:354386] Schmidt, EE, 2008-06-18 04:45:12
[InstanceEdit:384350] Kanapin, AA, 2008-11-26 14:00:39
[InstanceEdit:392885] Kanapin, AA, 2009-03-09 12:07:18
[InstanceEdit:400710] Schmidt, EE, 2009-03-25 05:33:35
[InstanceEdit:423310] Kanapin, AA
[InstanceEdit:435478] Kanapin, AA
[InstanceEdit:435871] Kanapin, AA
[InstanceEdit:447347] Kanapin, AA
[InstanceEdit:525883] Kanapin, AA
[InstanceEdit:613449] Kanapin, AA
[InstanceEdit:797602] Kanapin, AA
[InstanceEdit:937368] Yung, CK
[InstanceEdit:1042053] Yung, CK
[InstanceEdit:1220657] Yung, CK
[InstanceEdit:1300696] Yung, CK
[InstanceEdit:1301627] Yung, CK
[InstanceEdit:1551960] Weiser, JD
[InstanceEdit:1995863] Weiser, JD
[InstanceEdit:2132304] Weiser, JD
[InstanceEdit:2265580] Weiser, JD
[InstanceEdit:2455454] Weiser, JD
[InstanceEdit:3445779] Weiser, JD
[InstanceEdit:4341137] Weiser, JD
[InstanceEdit:5433710] Weiser, JD
[InstanceEdit:5618415] Weiser, JD
[InstanceEdit:5634237] Weiser, JD
[InstanceEdit:5673015] Weiser, JD
[InstanceEdit:8987656] Weiser, JD
[InstanceEdit:9037114] Weiser, JD
[InstanceEdit:9637257] Weiser, JD
[InstanceEdit:9657908] Weiser, JD
[InstanceEdit:9676415] Weiser, JD
[InstanceEdit:9715482] Weiser, JD
[InstanceEdit:9750299] Weiser, JD
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9862192] Weiser, Joel, 2024-02-26
[InstanceEdit:9917590] Weiser, Joel, 2024-08-09
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
nameSTRA6
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8991006] ENSEMBL:ENSG00000137868 STRA6 [Homo sapiens]
secondaryIdentifierSTRA6_HUMAN
A8K7F1
B7Z5M9
B7Z862
D3DW54
F5GYI8
I3L1G8
Q6PJF8
Q71RB9
Q7L9G1
Q7Z3U9
Q8TB21
Q9BX78
Q9H9U8
sequenceLength667
species[Species:48887] Homo sapiens
(isoformParent)[ReferenceIsoform:249778] UniProt:Q9BX79-2 STRA6 [Homo sapiens]
[ReferenceIsoform:249779] UniProt:Q9BX79-3 STRA6 [Homo sapiens]
[ReferenceIsoform:249780] UniProt:Q9BX79-4 STRA6 [Homo sapiens]
[ReferenceIsoform:413477] UniProt:Q9BX79-1 STRA6 [Homo sapiens]
[ReferenceIsoform:8975356] UniProt:Q9BX79-5 STRA6 [Homo sapiens]
[ReferenceIsoform:8975357] UniProt:Q9BX79-6 STRA6 [Homo sapiens]
(referenceEntity)[EntityWithAccessionedSequence:2453821] STRA6 T321P [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:2453826] STRA6 [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:2453830] STRA6 T644M [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:2453841] STRA6 P293L [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:2453845] STRA6 R655C [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:2453853] STRA6 P90L [plasma membrane] [Homo sapiens]
[EntityWithAccessionedSequence:2453887] STRA6 W23* [plasma membrane] [Homo sapiens]
(referenceSequence)[ReplacedResidue:2453810] L-threonine 644 replaced with L-methionine
[ReplacedResidue:2453828] L-proline 90 replaced with L-leucine
[ReplacedResidue:2453867] L-proline 293 replaced with L-leucine
[NonsenseMutation:2453868] Nonsense mutation at L-tryptophan 23
[ReplacedResidue:2453880] L-threonine 321 replaced with L-proline
[ReplacedResidue:2453908] L-arginine 655 replaced with L-cysteine
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No pathways have been reviewed or authored by UniProt:Q9BX79 STRA6 (249777)