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Details on Person UniProt:Q9Y6R1-3 SLC4A4

Class:IdReferenceIsoform:247290
_chainChangeLogchain:1-1079 added on Fri February 6 2015
_displayNameUniProt:Q9Y6R1-3 SLC4A4
_timestamp2026-02-20 21:53:46
chainchain:1-1079
checksum14B981A94DD64293
commentFUNCTION Electrogenic sodium/bicarbonate cotransporter with a Na(+):HCO3(-) stoichiometry varying from 1:2 to 1:3. May regulate bicarbonate influx/efflux at the basolateral membrane of cells and regulate intracellular pH.CATALYTIC ACTIVITY 2 hydrogencarbonate(out) + Na(+)(out) = 2 hydrogencarbonate(in) + Na(+)(in)CATALYTIC ACTIVITY 3 hydrogencarbonate(out) + Na(+)(out) = 3 hydrogencarbonate(in) + Na(+)(in)CATALYTIC ACTIVITY 2 hydrogencarbonate(out) + Na(+)(out) = 2 hydrogencarbonate(in) + Na(+)(in)CATALYTIC ACTIVITY 3 hydrogencarbonate(out) + Na(+)(out) = 3 hydrogencarbonate(in) + Na(+)(in)SUBUNIT Homodimer (PubMed:29500354). Interacts with CA2/carbonic anhydrase 2 and CA4/carbonic anhydrase 4 which may regulate transporter activity (PubMed:12411514, PubMed:14567693, PubMed:15218065, PubMed:15563508). Isoform 1 but not isoform 2 interacts with AHCYL1 (via PEST domain when phosphorylated); the interaction increases SLC4A4 isoform 1 activity (PubMed:16769890). Interacts with AHCYL2 (By similarity).SUBCELLULAR LOCATION Expressed in the corneal endothelium cells (at protein level). Expressed in pancreas and to a lower extent in heart, skeletal muscle, liver, parotid salivary glands, prostate, colon, stomach, thyroid, brain and spinal cord.TISSUE SPECIFICITY Specifically expressed in kidney at the level of proximal tubules.PTM Phosphorylation of Ser-1026 by PKA increases the binding of CA2 and changes the Na(+):HCO3(-) stoichiometry of the transporter from 3:1 to 2:1 (PubMed:11744745, PubMed:12411514, PubMed:12730338). Phosphorylated in presence of STK39 and dephosphorylated in presence of PP1 phosphatase; phosphorylation seems to inhibit SLC4A4 activity (By similarity).PTM N-glycosylated. May not be necessary for the transporter basic functions.DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE Loss of interaction with and stimulation by CA4 is the cause of retinitis pigmentosa type 17 (RP17).SIMILARITY Belongs to the anion exchanger (TC 2.A.31) family.
created[InstanceEdit:217385] Schmidt, EE, 2008-03-27 06:23:53
descriptionrecommendedName: Electrogenic sodium bicarbonate cotransporter 1 shortName: Sodium bicarbonate cotransporter alternativeName: Na(+)/HCO3(-) cotransporter alternativeName: Solute carrier family 4 member 4 alternativeName: kNBC1
geneNameSLC4A4
NBC
NBC1
NBCE1
identifierQ9Y6R1
isoformParent
isSequenceChangedFALSE
keyword3D-structure
Alternative splicing
Cell membrane
Disease variant
Glycoprotein
Ion transport
Membrane
Phosphoprotein
Proteomics identification
Reference proteome
Retinitis pigmentosa
Sodium
Sodium transport
Symport
Transmembrane
Transmembrane helix
Transport
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9948485] Weiser, Joel, 2025-05-21
[InstanceEdit:9983091] Weiser, Joel, 2026-02-20
nameSLC4A4
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:8996249] ENSEMBL:ENSG00000080493 SLC4A4 [Homo sapiens]
secondaryIdentifierS4A4_HUMAN
C4B714
O15153
Q8NEJ2
Q9H262
Q9NRZ1
Q9UIC0
Q9UIC1
Q9UP50
sequenceLength1079
species[Species:48887] Homo sapiens
variantIdentifierQ9Y6R1-3
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