Reactome: A Curated Pathway Database
THIS SITE IS USED FOR CURATION AND TESTING
IT IS NOT STABLE, IS LINKED TO AN INCOMPLETE DATA SET, AND IS NOT MONITORED FOR PERFORMANCE. WE STRONGLY RECOMMEND THE USE OF OUR PUBLIC SITE

Query author contributions in Reactome

Reactome depends on collaboration between our curation team and outside experts to assemble and peer-review its pathway modules. The integration of ORCID within Reactome enables us to meet a key challenge with authoring, curating and reviewing biological information by incentivizing and crediting the external experts that contribute their expertise and time to the Reactome curation process. More information is available at ORCID and Reactome.

If you have an ORCID ID that is not listed on this page, please forward this information to us and we will update your Reactome pathway records.

Name Email address

Details on Person UniProt:A7Z064 HMGCR

Class:IdReferenceGeneProduct:2455458
_chainChangeLogchain:1-888 added on Fri February 6 2015
_displayNameUniProt:A7Z064 HMGCR
_timestamp2025-02-21 18:47:28
chainchain:1-888
checksum16CFA777C3AA9D1A
commentFUNCTION Catalyzes the conversion of (3S)-hydroxy-3-methylglutaryl-CoA (HMG-CoA) to mevalonic acid, the rate-limiting step in the synthesis of cholesterol and other isoprenoids, thus plays a critical role in cellular cholesterol homeostasis.CATALYTIC ACTIVITY (R)-mevalonate + 2 NADP(+) + CoA = (3S)-3-hydroxy-3-methylglutaryl-CoA + 2 NADPH + 2 H(+)ACTIVITY REGULATION Regulated by a negative feedback mechanism through sterols and non-sterol metabolites derived from mevalonate (By similarity). Phosphorylation at Ser-872 down-regulates the catalytic activity (By similarity).PATHWAY Metabolic intermediate biosynthesis; (R)-mevalonate biosynthesis; (R)-mevalonate from acetyl-CoA: step 3/3.SUBUNIT Homotetramer. Homodimer (By similarity). Interacts (via its SSD) with INSIG1; the interaction, accelerated by sterols, leads to the recruitment of HMGCR to AMFR/gp78 for its ubiquitination by the sterol-mediated ERAD pathway. Interacts with UBIAD1 (By similarity).SUBCELLULAR LOCATION Undergoes sterol-mediated ubiquitination and ER-associated degradation (ERAD). Accumulation of sterols in the endoplasmic reticulum (ER) membrane, triggers binding of the reductase to the ER membrane protein INSIG1 or INSIG2. The INSIG1 binding leads to the recruitment of the ubiquitin ligase, AMFR/gp78, RNF139 or RNF145, initiating ubiquitination of the reductase. The ubiquitinated reductase is then extracted from the ER membrane and delivered to cytosolic 26S proteosomes by a mechanism probably mediated by the ATPase Valosin-containing protein VCP/p97. The INSIG2-binding leads to the recruitment of the ubiquitin ligase RNF139, initiating ubiquitination of the reductase. Lys-248 is the main site of ubiquitination. Ubiquitination is enhanced by the presence of a geranylgeranylated protein.PTM N-glycosylated. Deglycosylated by NGLY1 on release from the endoplasmic reticulum (ER) in a sterol-mediated manner.PTM Phosphorylated. Phosphorylation at Ser-872 reduces the catalytic activity.SIMILARITY Belongs to the HMG-CoA reductase family.
created[InstanceEdit:2455454] Weiser, JD
descriptionrecommendedName: 3-hydroxy-3-methylglutaryl-coenzyme A reductase shortName: HMG-CoA reductase ecNumber evidence="2"1.1.1.34
geneNameHMGCR
identifierA7Z064
isSequenceChangedFALSE
keywordCholesterol biosynthesis
Cholesterol metabolism
Endoplasmic reticulum
Glycoprotein
Isopeptide bond
Lipid biosynthesis
Lipid metabolism
Membrane
NADP
Oxidoreductase
Peroxisome
Phosphoprotein
Reference proteome
Steroid biosynthesis
Steroid metabolism
Sterol biosynthesis
Sterol metabolism
Transmembrane
Transmembrane helix
Ubl conjugation
modified[InstanceEdit:2587579] Weiser, JD
[InstanceEdit:5433710] Weiser, JD
[InstanceEdit:5618415] Weiser, JD
[InstanceEdit:5634237] Weiser, JD
[InstanceEdit:5673015] Weiser, JD
[InstanceEdit:9037114] Weiser, JD
[InstanceEdit:9607352] Weiser, JD
[InstanceEdit:9627708] Weiser, JD
[InstanceEdit:9637257] Weiser, JD
[InstanceEdit:9657908] Weiser, JD
[InstanceEdit:9676415] Weiser, JD
[InstanceEdit:9698430] Weiser, JD
[InstanceEdit:9706439] Weiser, JD
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9939033] Weiser, Joel, 2025-02-21
nameHMGCR
referenceDatabase[ReferenceDatabase:2] UniProt
secondaryIdentifierHMDH_BOVIN
F1MMP6
sequenceLength888
species[Species:48898] Bos taurus
[Change default viewing format]
No pathways have been reviewed or authored by UniProt:A7Z064 HMGCR (2455458)