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Details on Person UniProt:Q96FX8 PERP

Class:IdReferenceGeneProduct:242420
_chainChangeLogchain:1-193 added on Sat February 7 2015
_displayNameUniProt:Q96FX8 PERP
_timestamp2025-05-21 21:32:17
chainchain:1-193
checksum69654E35C53B3FCE
commentFUNCTION Component of intercellular desmosome junctions (By similarity). Plays a role in stratified epithelial integrity and cell-cell adhesion by promoting desmosome assembly (By similarity). Thereby plays a role in barrier function of the skin against infection (By similarity). Plays a role in mammary epithelial tissue homeostasis and remodeling during and after pregnancy, potentially via its involvement in desmosome cell-cell junctions (By similarity). Required for tooth enamel development via facilitating desmosome-mediated ameloblast adhesion to the stratum intermedium during the transitional stage of amelogenesis (By similarity). May also play a role in downstream transcriptional regulation of other genes involved in amelogenesis such as AMBN, ENAM, MMP20 and KLK4 (By similarity). Plays a role as an effector in the TP53-dependent apoptotic pathway (By similarity). Positively regulates apoptosis in T-helper 17 (Th17) cell populations via caspase-dependent signaling (By similarity). Promotes neutrophil transepithelial migration in response to chemoattractants such as hepoxilin A3 (HXA3), N-Formylmethionyl-leucyl-phenylalanine (fMLP) and CXCL8/IL-8 (PubMed:25486861). Required for neutrophil transepithelial migration in response to S.typhimurium infection (PubMed:25486861). May act as a positive regulator of endothelial cell apoptosis in response to blood flow-derived shear stress (By similarity).SUBUNIT (Microbial infection) Interacts with S.typhimurium sipA and sctB1/sipC.INTERACTION Associated with desmosomes (By similarity). Colocalizes with KRT14 in the cell membrane (PubMed:31898316). Clusters in a punctate pattern throughout the epithelial cytoplasm, in response to S.typhimurium infection (PubMed:25486861).TISSUE SPECIFICITY Expressed in skin, heart, placental, liver, pancreas, keratinocytes and dermal fibroblasts. May translocate to the intestinal apical epithelial cell surface via sipA and sctB1/sipC-promoted exocytic translocation following infection by S. Typhimurium (PubMed:25486861, PubMed:27078059).DISEASE The disease is caused by variants affecting the gene represented in this entry.DISEASE The disease is caused by variants affecting the gene represented in this entry.SIMILARITY Belongs to the TMEM47 family.
created[InstanceEdit:217385] Schmidt, EE, 2008-03-27 06:23:53
descriptionrecommendedName: fullName evidence="17"p53 apoptosis effector related to PMP-22 alternativeName: fullName evidence="14"Keratinocyte-associated protein 1 shortName evidence="14"KCP-1 alternativeName: fullName evidence="15"P53-induced protein PIGPC1 alternativeName: fullName evidence="13"Transmembrane protein THW
geneNamePERP
KCP1
KRTCAP1
PIGPC1
THW
identifierQ96FX8
isSequenceChangedFALSE
keywordApoptosis
Cell adhesion
Cell junction
Cell membrane
Cytoplasm
Disease variant
Membrane
Palmoplantar keratoderma
Proteomics identification
Reference proteome
Transmembrane
Transmembrane helix
modified[InstanceEdit:9836292] Weiser, Joel, 2023-05-25
[InstanceEdit:9852000] Weiser, Joel, 2023-11-03
[InstanceEdit:9917590] Weiser, Joel, 2024-08-09
[InstanceEdit:9926675] Weiser, Joel, 2024-11-03
[InstanceEdit:9948485] Weiser, Joel, 2025-05-21
namePERP
referenceDatabase[ReferenceDatabase:2] UniProt
referenceGene[ReferenceDNASequence:6800814] ENSEMBL:ENSG00000112378 PERP [Homo sapiens]
secondaryIdentifierPERP_HUMAN
B2RB73
E1P590
Q8IWS3
Q8N1J6
Q8NC16
Q9H1C5
Q9H230
sequenceLength193
species[Species:48887] Homo sapiens
(referenceEntity)[EntityWithAccessionedSequence:6800837] PERP [plasma membrane] [Homo sapiens]
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No pathways have been reviewed or authored by UniProt:Q96FX8 PERP (242420)